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Treatment is by oral carnitine administration

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In addition, in a pig model, Lactobacillus reuteri XL0930 in the gut microbiota reduced muscle carnitine levels and promoted fatty acid deposition by downregulating SLC22A5 in muscle tissue [253]

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Yet, LDH activity alone cannot provide sufficient cytosolic NAD+, and through lactate secretion glucose carbon is lost for biomolecule synthesis (DeBerardinis et al., 2008)
